Tehran University of Medical Sciences Current Journal of Neurology 2717-011X 12 2 2013 06 15 69 71 Farhad Assarzadegan Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Elaheh Ehsanpour Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran Behnam Hosseini Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran Nahid Beladi-Moghadam Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran Behnam Mansouri Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran Omid Hesami Imam Hossein Hospital, Department of Neurology, Shahid Beheshti University of Medical Sciences, Tehran, Iran 2015 10 14 Superficial siderosis (SS) is a rare disease which affects people in all ages and both sexes, but three times more in men. Pathological etiology is deposition of hemosiderin (a product of the breakdown of blood) in leptomeninges, subpial layer, ependymal surface and other parts of central nervous system (CNS) and typically leads to neurological dysfunction and progressive irreversible signs and symptoms. We present a 33-year-old man with complete deafness in left ear, partial hearing loss in right ear, gait imbalance, bilateral frontotemporal throbbing headache and anosmia resulted from superficial siderosis. https://ijnl.tums.ac.ir/index.php/ijnl/article/view/658 https://ijnl.tums.ac.ir/index.php/ijnl/article/download/658/144