Tehran University of Medical Sciences Current Journal of Neurology 2717-011X 11 3 2012 09 15 115 117 Abbas Tafakhori Iranian Center of Neurological Research, Department of Neurology, Tehran University of Medical Sciences Imam Khomeini Hospital, Tehran, Iran. Mohammad Salehi Sadaghiani Iranian Center of Neurological Research, Department of Neurology, Tehran University of Medical Sciences Imam Khomeini Hospital, Tehran, Iran Mohammad Hossein Harirchian Iranian Center of Neurological Research, Department of Neurology, Tehran University of Medical Sciences Imam Khomeini Hospital, Tehran, Iran Zeinab Taheri Iranian Center of Neurological Research, Department of Neurology, Tehran University of Medical Sciences Imam Khomeini Hospital, Tehran, Iran Vajiheh Aghamollaii Iranian Center of Neurological Research, Department of Neurology, Tehran University of Medical Sciences Imam Khomeini Hospital, Tehran, Iran 2015 10 17 Background: Paget's disease is a focal bone disorder manifested as bone overgrowth and disrupted bone integrity as a result of accelerated bone remodelling rate. Rarely, Paget's disease of the base of the skull results in hydrocephalic dementia, and the triad of normal pressure hydrocephalus syndrome is a much more scarce entity. Case Report: Herein, we report an elderly woman who presented in Imam Khomeini Hospital, Tehran, Iran, with normal pressure hydrocephalus syndrome due to Paget's bone disease. Furthermore, we have reviewed relevant previous studies. Conclusion: Paget's disease can be presented as normal pressure hydrocephalus syndrome. https://ijnl.tums.ac.ir/index.php/ijnl/article/view/793 https://ijnl.tums.ac.ir/index.php/ijnl/article/download/793/66